Tabla 3 Clasificación
da las vasculitis en relación al tamaño del vaso afecto

Types of
vessels that are defined as large vessels (A), medium vessels (B), and small
vessels (C) in the Chapel Hill Consensus Conference nomenclature system. The
kidney is used to exemplify medium and small vessels. Large vessels are the
aorta and its major branches and the analogous veins. Medium vessels are the
main visceral arteries and veins and their initial branches. Small vessels are
intraparenchymal arteries, arterioles, capillaries, venules, and veins.

Distribution
of vessel involvement by large vessel vasculitis, medium vessel vasculitis, and
small vessel vasculitis. Note that there is substantial overlap with respect to
arterial involvement, and an important concept is that all 3 major categories of
vasculitis can affect any size artery. Large vessel vasculitis affects large
arteries more often than other vasculitides. Medium vessel vasculitis
predominantly affects medium arteries. Small vessel vasculitis predominantly
affects small vessels, but medium arteries and veins may be affected, although
immune complex small vessel vasculitis rarely affects arteries. Not shown is
variable vessel vasculitis, which can affect any type of vessel, from aorta to
veins. The diagram depicts (from left to right) aorta, large artery, medium
artery, small artery/arteriole, capillary, venule, and vein. Anti-GBM = anti–glomerular
basement membrane; ANCA = antineutrophil cytoplasmic antibody.
|
De pequeño vaso |
vasculitis que afecta
predominantemente a vasos de pequeño tamaño incluyendo areterias
intraparenquimatosas, arteriolas, capilares y venulas. |
Vasculitis asociadas a
ANCA
Vasculitis por
inmunocomplejos
Vasculitis
crioglobulinemica
Vasculitis por IgA
Vasculitis
hipocomplementémica |
vasculitis de vasos
variables |
incluye las vasculitis
sin predominancia por afectar a un tipo de vaso |
Enfermedad de Behçet
Vasculitis del
síndrome deCogan |