Tabla 3 Clasificación da las vasculitis en relación al tamaño del vaso afecto

 

Types of vessels that are defined as large vessels (A), medium vessels (B), and small vessels (C) in the Chapel Hill Consensus Conference nomenclature system. The kidney is used to exemplify medium and small vessels. Large vessels are the aorta and its major branches and the analogous veins. Medium vessels are the main visceral arteries and veins and their initial branches. Small vessels are intraparenchymal arteries, arterioles, capillaries, venules, and veins.

 

 Distribution of vessel involvement by large vessel vasculitis, medium vessel vasculitis, and small vessel vasculitis. Note that there is substantial overlap with respect to arterial involvement, and an important concept is that all 3 major categories of vasculitis can affect any size artery. Large vessel vasculitis affects large arteries more often than other vasculitides. Medium vessel vasculitis predominantly affects medium arteries. Small vessel vasculitis predominantly affects small vessels, but medium arteries and veins may be affected, although immune complex small vessel vasculitis rarely affects arteries. Not shown is variable vessel vasculitis, which can affect any type of vessel, from aorta to veins. The diagram depicts (from left to right) aorta, large artery, medium artery, small artery/arteriole, capillary, venule, and vein. Anti-GBM = anti–glomerular basement membrane; ANCA = antineutrophil cytoplasmic antibody.

De Gran Vaso

Vasculitis que afecta a vasos de gran tamaño en mayor medida que otras formas de vasculitis

Arteritis de células gigantes

Arteritis de Takayasu

De mediano vaso

Vasculitis que afecta predominantemente a arterias de mediano tamaño, comprendiendo las areterias viscerales más importante y sus ramificaciones

PAN
Síndrome de Kawasaki

De pequeño vaso

vasculitis que afecta predominantemente a vasos de pequeño tamaño incluyendo areterias intraparenquimatosas, arteriolas, capilares y venulas.

Vasculitis asociadas a ANCA

  • Anca con especificidad a mieloperoxidasa

  • Anca con especificidad a proteinasa 3

  • Anca negativo

Vasculitis por inmunocomplejos

Vasculitis crioglobulinemica

Vasculitis por IgA

Vasculitis hipocomplementémica

vasculitis de vasos variables

incluye las vasculitis sin predominancia por afectar a un tipo de vaso

Enfermedad de Behçet

Vasculitis del síndrome deCogan

vasculitis de organo único vasculitis en arterias o venas de cualquier tamaño que no tiene hallazgos que indiquen que es la expresión limitada de una vasculitis sistemica. El órgano afecto  y el vaso deben consstar en el nombre (vasculitis cutanea de pequeño vaso)

 

 

 

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